Total Intravenous Anesthesia for a Patient with Progressive Muscular Dystrophy.

Total intravenous anesthesia for aortic aneurysm replacement surgery in a patient with limb-girdle dystrophy.

We report the anesthetic management with total intravenous anesthesia of a 61-year-old male diagnosed with limb-girdle muscular dystrophy admitted for replacement of ascending aorta due to an aortic aneurysm. Limb-girdle muscular dystrophy belongs to a genetically heterogeneous group of muscular dystrophies involving shoulder and hip girdles. Although the risk of malignant hyperthermia does not...

Total Intravenous Anesthesia for a Patient with Narcolepsy

Narcolepsy is a disorder of unknown etiology. It is characterized by excessive sleepiness that is typically associated with cataplexy and other Rapid Eye Movement (REM) sleep phenomena, such as sleep paralysis and hypnagogic hallucinations. When administering general anesthesia to patients with narcolepsy, delayed emergence after general anesthesia, post-operative hypersomnia and drug interacti...

[Progressive muscular dystrophy].

This paper describes the case of a young man with progressive muscular dystrophy who had supraventricular arrhythmias and intractable congestive failure. Hemodynamic studies and left cineventriculographic findings were compatible with a diagnosis of severe left ventricular failure. Coronary cinearteriography showed an abrupt ending of the artery to the sino-atrial node. At necropsy, a noninflam...

Progressive Muscular Dystrophy (Erb.)

Total intravenous anesthesia in a 10-month-old patient with congenital myotonic dystrophy undergoing endoscopic third ventriculostomy -A case report-

Myotonic dystrophy is a rare genetic disorder characterized by muscle atrophy and weakness. Surgical treatment of this condition poses various problems for the anesthesiologist. We describe the anesthetic management of a 10-month-old infant with congenital myotonic dystrophy, who was scheduled for endoscopic third ventriculostomy under general anesthesia. Anesthesia was induced with thiopental ...